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318 results are found.
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enzyme
GDH 2
Glutamate dehydrogenase 2, mitochondrial
enzyme
Glutamine N-acyltransferase
Glycine N-acyltransferase-like protein 1
enzyme
Proline oxidase
Proline dehydrogenase 1, mitochondrial
enzyme
SHMT
Serine hydroxymethyltransferase, mitochondrial
enzyme
AKB ligase
2-amino-3-ketobutyrate coenzyme A ligase, mitochondrial
enzyme
GCVT
Aminomethyltransferase, mitochondrial
enzyme
Glycine decarboxylase
Glycine dehydrogenase
enzyme
BCAT(m)
Branched-chain-amino-acid aminotransferase, mitochondrial
enzyme
BCKD-kinase
[3-methyl-2-oxobutanoate dehydrogenase [lipoamide]] kinase, mitochondrial
enzyme
IBDH
Isobutyryl-CoA dehydrogenase, mitochondrial
enzyme
HIBADH
3-hydroxyisobutyrate dehydrogenase, mitochondrial
enzyme
MMSDH
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
enzyme
AadAT
Kynurenine/alpha-aminoadipate aminotransferase, mitochondrial
enzyme
LKR/SDH
Alpha-aminoadipic semialdehyde synthase, mitochondrial
enzyme
Alanine--glyoxylate aminotransferase 2-like 2
5-phosphohydroxy-L-lysine phospho-lyase
enzyme
GDH 1
Glutamate dehydrogenase 1, mitochondrial
enzyme
Ornithine delta-aminotransferase
Ornithine aminotransferase, mitochondrial
enzyme
GLS
Glutaminase liver isoform, mitochondrial
enzyme
OTCase
Ornithine carbamoyltransferase, mitochondrial
enzyme
Aldehyde dehydrogenase family 5 member A1
Succinate-semialdehyde dehydrogenase, mitochondrial
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